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Epidermolysis Bullosa - An anaesthetic challenge

Authors:

Lokvendra Singh Budania,

Kasturba Medical College, Manipal, IN
About Lokvendra Singh
Associate Professor
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M. V. Eeshwar ,

Kasturba Medical College, Manipal, IN
About M. V.
Assistant Professor
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Vamshidhar Chamala Reddy,

Kasturba Medical College, Manipal, IN
About Vamshidhar Chamala
Assistant professor
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Yogesh K. Gaude,

Kasturba Medical College, Manipal, IN
About Yogesh K.
Associate professor 
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Sai Anand,

Kasturba Medical College, Manipal, IN
About Sai
Junior resident
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Anshu Sharma

Central institute of psychiatry, IN
About Anshu
Assistant professor
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Abstract

Epidermolysis bullosa (EB) is a rare genetic disorder characterized by blisters of skin and mucosa as a result of friction or minor trauma. EB can be of three forms: Epidermolysis Simplex (EBS), Junctional Epidermolysis Bullosa (JEB) and Dystrophic (DEB). Management of EB poses a challenge to the anesthetist. We report a case of 4-year-old girl who had been diagnosed with DEB since birth. At present, she was diagnosed to have esophageal stricture and was posted for balloon dilatation of esophagus. Airway examination revealed mouth opening of 1.5-2 fingers breadth with adequate neck movements. Difficult airway was anticipated. General anesthesia was administered and intubation was achieved using Airtraq video laryngoscope. Care was taken not to cause further trauma to the skin and mucosa in the perioperative period.
How to Cite: Budania, L.S., Eeshwar, M.V., Reddy, V.C., Gaude, Y.K., Anand, S. and Sharma, A., 2019. Epidermolysis Bullosa - An anaesthetic challenge. Sri Lankan Journal of Anaesthesiology, 27(2), pp.163–165. DOI: http://doi.org/10.4038/slja.v27i2.8405
Published on 25 Jul 2019.
Peer Reviewed

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